A 30-year-old male presented to the emergency department with ataxic gait, double vision, and tingling in his extremities that began 11 days after an upper respiratory infection. His physical examination revealed ophthalmoplegia, dysmetria, reduced sensation to light touch, temperature, and vibration in his distal extremities, and an unsteady gait with a positive Romberg sign. Despite unremarkable MRI scans of his orbits, brain, and spine, and normal EMG and lumbar puncture results, elevated serum Ganglioside GQ1b antibodies with a titer of 1:128000 confirmed a diagnosis of Guillain-Barré syndrome, Miller Fisher variant. The patient underwent five days of IVIG treatment, showing gradual symptom improvement, and reported near-complete resolution one week post-discharge.