Stroke can occur at any age; however, it shows a higher incidence during adulthood, most of the  time in the pediatric population the expression is atypical and unusual. Among the causes of stroke in children, cardioembolic mechanisms are rare, atrial myxoma representing an exceptional (<0.28%). The present case illustrates a devastating ischemic stroke as an initial manifestation of a cardiac neoplasm in a pediatric patient.

Cardiac myxoma is accepted as an uncommon cause of stroke in the pediatric population. We emphasized the importance of the typical triad (cardiac obstructive symptoms, constitutional manifestations  and embolic phenomena) that  can appear in >30% of cases. The incidence is 2 per 100,000 children per year, and the stroke presentation is  rare as a  first presentation. Previous reports elucidate the prognosis is generally favorable specially when the early diagnosis and surgical resection are performed. 

The current medical literature is remarkable in demonstrating limited information about myxoma incidence in the pediatric population.  Also the importance in establishing  a collaborative interaction between Paediatricians, Cardiologists and Neurologists.